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J. Erdheim. Medionecrosis aortae idiopathica (cystica). Archiv fĂĽr pathologische
Anatomie und Physiologie und fĂĽr klinische Medizin, 1929, 273: 454-479.
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correlate of familial thoracic aortic aneurysms. The image shows abundant basophilic ground substance in the
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The term "cystic medial degeneration" is sometimes used instead of "cystic medial necrosis", because
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GeneReview/NCBI/NIH/UW entry on
Thoracic Aortic Aneurysms and Aortic Dissections
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It is sometimes called "Erdheim cystic medial necrosis of aorta", after
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There is an association between familial thoracic aortic aneurysm and
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caused by aging contributes to weakening of the wall of the artery.
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66:(blue at top of image) and disruption of the elastic fibers. The
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In the aorta, this can result in the formation of a fusiform
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Familial aortic dissection, cystic medial necrosis of aorta
105:
as well as other hereditary connective tissue disorders.
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1079:Chronic cerebrospinal venous insufficiency
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352:http://www.emedicine.com/emerg/topic28.htm
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58:showing cystic medial degeneration, the
14:
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331:
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851:Hereditary hemorrhagic telangiectasia
487:
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856:Generalized essential telangiectasia
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336:Online Mendelian Inheritance in Man
326:
24:
132:. There is also increased risk of
25:
1296:
387:
85:Familial thoracic aortic aneurysm
70:(yellow at bottom of image) with
33:Familial thoracic aortic aneurysm
1006:Cerebral venous sinus thrombosis
269:
230:
957:Hepatic veno-occlusive disease
374:
357:
344:
300:
13:
1:
769:Aneurysm of sinus of Valsalva
623:Monckeberg's arteriosclerosis
319:
1074:Chronic venous insufficiency
699:Aortoiliac occlusive disease
261:
222:
113:A degenerative breakdown of
7:
1089:Inferior vena cava syndrome
1084:Superior vena cava syndrome
811:Vertebral artery dissection
801:Intracranial berry aneurysm
139:
10:
1301:
1190:Hypertensive heart disease
841:Arteriovenous malformation
816:Familial aortic dissection
1245:
1215:Renovascular hypertension
1180:
1171:
1158:Hepatic artery thrombosis
1106:
1066:
1021:
925:
907:
898:
866:
826:
806:Carotid artery dissection
759:Abdominal aortic aneurysm
731:
691:
668:
609:Intermittent claudication
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572:Peripheral artery disease
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540:
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450:
395:
54:
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37:
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1200:Hypertensive nephropathy
1013:Post-thrombotic syndrome
994:Paget–Schroetter disease
786:Coronary artery aneurysm
764:Thoracic aortic aneurysm
1285:Cardiogenetic disorders
1255:Orthostatic hypotension
1237:White coat hypertension
714:Fibromuscular dysplasia
678:Carotid artery stenosis
1227:Pulmonary hypertension
1210:Secondary hypertension
1205:Essential hypertension
1195:Hypertensive emergency
1036:Portacaval anastomosis
972:Portal vein thrombosis
614:Critical limb ischemia
515:Cardiovascular disease
278:This section is empty.
239:This section is empty.
18:Cystic medial necrosis
1280:Diseases of the aorta
1232:Systolic hypertension
977:Renal vein thrombosis
836:Arteriovenous fistula
828:Vascular malformation
796:Intracranial aneurysm
683:Renal artery stenosis
316:is not always found.
1146:Paradoxical embolism
1141:Cholesterol embolism
967:May–Thurner syndrome
962:Budd–Chiari syndrome
945:Deep vein thrombosis
940:primarily lower limb
719:Raynaud's phenomenon
1222:Benign hypertension
350:Wiesenfarth, John,
1136:Pulmonary embolism
1046:Esophageal varices
984:upper limb / torso
628:Arteriolosclerosis
451:External resources
109:Signs and symptoms
94:disorder of large
1267:
1266:
1263:
1262:
1107:Arteries or veins
1102:
1101:
927:Venous thrombosis
894:
893:
876:Cherry hemangioma
776:Aortic dissection
727:
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562:Buerger's disease
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354:, October 4, 2005
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134:aortic dissection
82:
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68:tunica adventitia
27:Medical condition
16:(Redirected from
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989:Mondor's disease
932:Thrombophlebitis
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581:Arteriosclerosis
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280:You can help by
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1124:Microangiopathy
1119:Macroangiopathy
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1031:Gastric varices
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754:Aortic aneurysm
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709:Erythromelalgia
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589:Atherosclerosis
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144:Types include:
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103:Marfan syndrome
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868:Vascular nevus
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742:pseudoaneurysm
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653:Oxycholesterol
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396:Classification
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1041:Caput medusae
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704:Degos disease
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370:Who Named It?
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307:Jakob Erdheim
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289:December 2017
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250:December 2017
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76:Movat's stain
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1182:Hypertension
1094:Venous ulcer
1000:
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909:Inflammation
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638:Hyperplastic
599:Fatty streak
542:Inflammation
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282:adding to it
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243:adding to it
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176:11q23.3-q24
143:
127:
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100:
84:
83:
72:vaso vasorum
64:tunica media
1247:Hypotension
791:head / neck
643:Cholesterol
533:capillaries
301:Terminology
38:Other names
1274:Categories
1163:Vasculitis
1153:Thrombosis
1114:Angiopathy
1058:Varicocele
1051:Hemorrhoid
881:Halo nevus
737:dissection
528:arterioles
436:DiseasesDB
320:References
60:histologic
56:Micrograph
917:Phlebitis
658:Trans fat
594:Foam cell
550:Arteritis
517:(vessels)
460:eMedicine
365:synd/2409
262:Treatment
223:Diagnosis
89:autosomal
1131:Embolism
733:Aneurysm
670:Stenosis
604:Atheroma
555:Aortitis
524:Arteries
465:emerg/28
338:(OMIM):
314:necrosis
140:Genetics
130:aneurysm
115:collagen
96:arteries
92:dominant
952:abdomen
633:Hyaline
119:elastin
430:607086
419:441.00
340:607086
205:611788
185:132900
170:607086
161:Locus
121:, and
87:is an
1067:Other
900:Veins
750:torso
692:Other
441:30073
211:ACTA2
201:AAT6
191:MYH11
181:AAT4
166:AAT1
158:Gene
150:Type
1001:head
531:and
425:OMIM
414:9-CM
216:10q
196:16p
154:OMIM
648:LDL
410:ICD
368:at
284:.
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328:^
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507:e
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493:v
412:-
402:D
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287:(
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248:(
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