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Incontinentia pigmenti achromians

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58: 78:. Though the consistency of the skin findings have led to the term "hypomelanosis of Ito", it actually refers to a group of disorders with various genetic causes including polyploidies and aneuploidies. Based upon the specifics of the genetic defect, the skin findings can be accompanied by a great range of systemic findings. These include central nervous system, ocular, and musculoskeletal defects. Nonetheless, the vast majority of cases are limited to the skin. As opposed to 91: 732: 1177: 941: 666: 279: 1153: 593: 661: 82:, hypomelanosis of Ito affects both genders equally. This disorder was first described by Japanese dermatologist Minoru Ito in 1952. 937: 676: 656: 651: 1048: 853: 1043: 878: 359: 868: 646: 272: 194: 144:"Studies on Melanin XI. Incontinentia pigmenti achromians. A single case of nevus depigmentosus systematicus bilaterlis" 74:") is a cutaneous condition characterized by various patterns of bilateral or unilateral hypopigmentation following the 873: 793: 1146: 578: 522: 129: 512: 996: 752: 265: 459: 858: 769: 588: 507: 1182: 958: 917: 863: 454: 1139: 1127: 825: 101: 912: 932: 598: 774: 722: 479: 474: 727: 205: 57: 1172: 788: 681: 424: 815: 671: 517: 96: 79: 17: 245: 927: 354: 333: 288: 951: 843: 382: 779: 8: 573: 338: 820: 747: 552: 547: 464: 434: 986: 922: 612: 469: 216: 125: 75: 42: 257: 737: 300: 155: 51: 160: 143: 1079: 799: 757: 742: 712: 686: 583: 429: 210: 1123: 1119: 1098: 1091: 1069: 991: 557: 497: 387: 221: 1166: 1017: 946: 907: 502: 784: 708: 1074: 1012: 240: 47: 1064: 1035: 981: 717: 536: 444: 377: 316: 292: 186: 626: 407: 631: 416: 325: 976: 848: 764: 704: 621: 402: 305: 92:
List of dental abnormalities associated with cutaneous conditions
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James, William; Berger, Timothy; Elston, Dirk (2005).
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Hypomelanosis of Ito, Linear nevoid hypopigmentation
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Andrews' Diseases of the Skin: Clinical Dermatology
733:Inherited patterned lentiginosis in black persons 1164: 942:Eczematid-like purpura of Doucas and Kapetanakis 1147: 594:Yemenite deaf-blind hypopigmentation syndrome 273: 662:Reticular pigmented anomaly of the flexures 1154: 1140: 280: 266: 56: 159: 938:Doucas and Kapetanakis pigmented purpura 667:Naegeli–Franceschetti–Jadassohn syndrome 1178:Genetic disorders with OMIM but no gene 677:X-linked reticulate pigmentary disorder 657:Reticulate acropigmentation of Kitamura 652:Pigmentatio reticularis faciei et colli 1165: 1049:Dyschromatosis universalis hereditaria 854:Familial progressive hyperpigmentation 114: 1044:Dyschromatosis symmetrica hereditaria 879:Transient neonatal pustular melanosis 261: 1113: 869:Photoleukomelanodermatitis of Kobori 647:Dermatopathia pigmentosa reticularis 141: 13: 874:Postinflammatory hyperpigmentation 794:Poikiloderma vasculare atrophicans 14: 1194: 579:Postinflammatory hypopigmentation 523:Progressive macular hypomelanosis 172: 68:Incontinentia pigmenti achromians 29:Incontinentia pigmenti achromians 513:Idiopathic guttate hypomelanosis 997:Titanium metallic discoloration 753:Partial unilateral lentiginosis 770:Erythema dyschromicum perstans 135: 1: 959:Hemosiderin hyperpigmentation 918:Pigmented purpuric dermatosis 864:Periorbital hyperpigmentation 360:Vogt–Koyanagi–Harada syndrome 161:10.1620/tjem.55.Supplement_34 107: 1126:. You can help Knowledge by 826:Shiitake mushroom dermatitis 102:List of cutaneous conditions 7: 913:Iron metallic discoloration 589:Vagabond's leukomelanoderma 85: 10: 1199: 1112: 859:Pallister–Killian syndrome 508:Albinism–deafness syndrome 15: 1057: 1034: 1005: 967: 900: 891: 834: 808: 775:Lichen planus pigmentosus 723:Centrofacial lentiginosis 695: 639: 620: 611: 566: 535: 490: 480:Griscelli syndrome type 3 475:Griscelli syndrome type 2 455:Hermansky–Pudlak syndrome 443: 415: 400: 368: 347: 324: 313: 299: 231: 180: 41: 33: 28: 728:Generalized lentiginosis 460:ChĂ©diak–Higashi syndrome 124:. (10th ed.). Saunders. 16:Not to be confused with 789:Poikiloderma of Civatte 425:Oculocutaneous albinism 933:Gougerot–Blum syndrome 816:Incontinentia pigmenti 672:Dyskeratosis congenita 599:Wende–Bauckus syndrome 518:Phylloid hypomelanosis 289:Pigmentation disorders 97:Incontinentia pigmenti 80:incontinentia pigmenti 18:Incontinentia pigmenti 355:Alezzandrini syndrome 334:Quadrichrome vitiligo 154:(Supplement): 57–59. 1183:Genodermatoses stubs 952:Angioma serpiginosum 844:Acanthosis nigricans 383:Waardenburg syndrome 72:hypomelanosis of Ito 682:Galli–Galli disease 574:Nevus depigmentosus 142:Ito, Minor (1952). 928:Majocchi's disease 821:Scratch dermatitis 748:Mucosal lentigines 548:Vasospastic macule 465:Griscelli syndrome 232:External resources 1135: 1134: 1107: 1106: 1030: 1029: 1026: 1025: 987:Arsenic poisoning 923:Schamberg disease 887: 886: 780:CafĂ© au lait spot 607: 606: 531: 530: 470:Elejalde syndrome 396: 395: 255: 254: 76:lines of Blaschko 65: 64: 23:Medical condition 1190: 1156: 1149: 1142: 1114: 898: 897: 738:Ink spot lentigo 637: 636: 618: 617: 413: 412: 339:Vitiligo ponctuĂ© 322: 321: 311: 310: 282: 275: 268: 259: 258: 178: 177: 166: 165: 163: 148:Tohoku J Exp Med 139: 133: 118: 70:(also known as " 61: 60: 52:medical genetics 26: 25: 1198: 1197: 1193: 1192: 1191: 1189: 1188: 1187: 1163: 1162: 1161: 1160: 1110: 1108: 1103: 1053: 1022: 1001: 969: 963: 908:Hemochromatosis 893: 883: 836: 830: 804: 800:Riehl melanosis 758:PUVA lentigines 743:Lentigo maligna 713:Lentigo simplex 697: 691: 687:Revesz syndrome 630: 625: 603: 584:Pityriasis alba 562: 553:Woronoff's ring 540: 527: 486: 447: 439: 430:Ocular albinism 406: 392: 370: 364: 343: 315: 304: 295: 286: 256: 251: 250: 227: 226: 189: 175: 170: 169: 140: 136: 119: 115: 110: 88: 55: 24: 21: 12: 11: 5: 1196: 1186: 1185: 1180: 1175: 1173:Genodermatoses 1159: 1158: 1151: 1144: 1136: 1133: 1132: 1120:Genodermatoses 1105: 1104: 1102: 1101: 1099:Depigmentation 1096: 1095: 1094: 1084: 1083: 1082: 1072: 1070:Skin whitening 1067: 1061: 1059: 1055: 1054: 1052: 1051: 1046: 1040: 1038: 1032: 1031: 1028: 1027: 1024: 1023: 1021: 1020: 1015: 1009: 1007: 1003: 1002: 1000: 999: 994: 992:Lead poisoning 989: 984: 979: 973: 971: 965: 964: 962: 961: 956: 955: 954: 949: 944: 935: 930: 925: 915: 910: 904: 902: 895: 889: 888: 885: 884: 882: 881: 876: 871: 866: 861: 856: 851: 846: 840: 838: 832: 831: 829: 828: 823: 818: 812: 810: 806: 805: 803: 802: 797: 791: 782: 777: 772: 767: 761: 760: 755: 750: 745: 740: 735: 730: 725: 720: 715: 701: 699: 693: 692: 690: 689: 684: 679: 674: 669: 664: 659: 654: 649: 643: 641: 634: 615: 609: 608: 605: 604: 602: 601: 596: 591: 586: 581: 576: 570: 568: 564: 563: 561: 560: 558:Nevus anemicus 555: 550: 544: 542: 533: 532: 529: 528: 526: 525: 520: 515: 510: 505: 500: 498:Cross syndrome 494: 492: 488: 487: 485: 484: 483: 482: 477: 472: 462: 457: 451: 449: 441: 440: 438: 437: 432: 427: 421: 419: 410: 398: 397: 394: 393: 391: 390: 388:Tietz syndrome 385: 380: 374: 372: 366: 365: 363: 362: 357: 351: 349: 345: 344: 342: 341: 336: 330: 328: 319: 308: 297: 296: 285: 284: 277: 270: 262: 253: 252: 249: 248: 236: 235: 233: 229: 228: 225: 224: 213: 202: 190: 185: 184: 182: 181:Classification 174: 173:External links 171: 168: 167: 134: 112: 111: 109: 106: 105: 104: 99: 94: 87: 84: 63: 62: 45: 39: 38: 35: 31: 30: 22: 9: 6: 4: 3: 2: 1195: 1184: 1181: 1179: 1176: 1174: 1171: 1170: 1168: 1157: 1152: 1150: 1145: 1143: 1138: 1137: 1131: 1129: 1125: 1122:article is a 1121: 1116: 1115: 1111: 1100: 1097: 1093: 1090: 1089: 1088: 1085: 1081: 1078: 1077: 1076: 1073: 1071: 1068: 1066: 1063: 1062: 1060: 1056: 1050: 1047: 1045: 1042: 1041: 1039: 1037: 1033: 1019: 1018:Tar melanosis 1016: 1014: 1011: 1010: 1008: 1004: 998: 995: 993: 990: 988: 985: 983: 980: 978: 975: 974: 972: 966: 960: 957: 953: 950: 948: 947:Lichen aureus 945: 943: 939: 936: 934: 931: 929: 926: 924: 921: 920: 919: 916: 914: 911: 909: 906: 905: 903: 899: 896: 890: 880: 877: 875: 872: 870: 867: 865: 862: 860: 857: 855: 852: 850: 847: 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849:Freckle 765:Melasma 705:Lentigo 622:Melanin 403:melanin 314:Loss of 306:leucism 211:D010859 1087:Tattoo 970:metals 835:Other/ 809:Linear 613:Hyper- 246:001461 200:300337 128:  54:  1118:This 1006:Other 968:Other 892:Other 491:Other 301:Hypo- 222:31154 1124:stub 901:Iron 206:MeSH 195:OMIM 126:ISBN 539:w/o 156:doi 1169:: 711:: 244:: 220:: 209:: 198:: 152:55 150:. 146:. 50:, 1155:e 1148:t 1141:v 1130:. 940:/ 796:) 787:( 707:/ 629:/ 624:/ 405:/ 303:/ 291:/ 281:e 274:t 267:v 187:D 164:. 158:: 132:. 20:.

Index

Incontinentia pigmenti
Specialty
Dermatology
medical genetics
Edit this on Wikidata
lines of Blaschko
incontinentia pigmenti
List of dental abnormalities associated with cutaneous conditions
Incontinentia pigmenti
List of cutaneous conditions
ISBN
0-7216-2921-0
"Studies on Melanin XI. Incontinentia pigmenti achromians. A single case of nevus depigmentosus systematicus bilaterlis"
doi
10.1620/tjem.55.Supplement_34
D
OMIM
300337
MeSH
D010859
DiseasesDB
31154
MedlinePlus
001461
v
t
e
Pigmentation disorders
Dyschromia
Hypo-

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